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The following articles, Power Points, and presentations were selected to help manage this disease; this will be continuously added to.
Pathophysiology of Childhood Polycystic Kidney Diseases: New Insights into Disease-Specific Therapy, PubMed
Clinical Courses and Complications of Young Adults with Autosomal Recessive Polycystic Kidney Disease (ARPKD), PMC, National Library of Medicine
Early Childhood Height-Adjusted Total Kidney Volume as a Risk Marker of Kidney Survival in ARPKD, PubMed
Polycystic Kidney Disease, Autosomal Recessive, Gene Reviews
Pediatric Polycystic Kidney Disease, Medscape, 2013
New approaches to the autosomal recessive polycystic kidney disease patient with dual kidney–liver complications, Pediatric Transplant, June, 2013
NIH Natural History Study Research Papers, resulting from our Natural History study.
Congenital Hepatic Fibrosis, U.S. National Library of Medicine, 2013
Congenital Hepatic Fibrosis Overview, GeneReviews, 2008
Congenital Hepatic Fibrosis, Medscape, 2013
Liver Disease in ARPKD by Benjamin L. Shneider
Experience of a single center with congenital hepatic fibrosis: A review of the literature, World Journal of Gastroenterology. 2010.
Successful long-term outcome of pediatric liver–kidney_Spain review 2017
Health-related quality of life after combined liver and kidney transplantation in children
Liver and Pancreas Transplantation Information from UCLA
Specific for UCLA, but holds information for all liver and pancreas transplant patients.
Looking for more disease-specific information? For peer-reviewed published medical literature, search PubMed.